Effects of CoQ10 Replacement Therapy on the Audiological Characteristics of Pediatric Patients with COQ6 Variants

Figure 1

Serial audiograms of 7 patients with biallelic COQ6 variants. Cases for whom serial audiograms were available for adequate periods after oral CoQ10 administration are shown. Patient 2 underwent left cochlear implantation immediately after the hearing test; the test performed immediately after surgery was excluded from analysis. R: right; L: left; y: years.