A Challenging Case of Genetically and Histologically Diagnosed Pulmonary Veno-Occlusive Disease with Extracorporeal Life Support and Redo Lung Transplantation

<div>Transthoracic echocardiography revealed severe dilatation and systolic dysfunction of the right ventricle while normal left ventricle and moderate pericardial effusion (a). There was severe TR with an estimated PASP &gt;80 mmHg and TRV 4.01 m/s (b). The right atrium was severely dilated with a small atrial septal defect (c). TEE revealed a positive agitated saline test confirming interatrial shunting (d).</div>

Case Reports in Cardiology

fig2

Figure 2

Figure 2: A Challenging Case of Genetically and Histologically Diagnosed Pulmonary Veno-Occlusive Disease with Extracorporeal Life Support and Redo Lung Transplantation 

Figure 2 | A Challenging Case of Genetically and Histologically Diagnosed Pulmonary Veno-Occlusive Disease with Extracorporeal Life Support and Redo Lung Transplantation 