“A Dangerous Black Box:” Idiopathic Hemophagocytic Lymphohistiocytosis in Adult Patients—A Case Report and Review of the Literature

Table 3

Saint-Antoine score [23] calculated for this case (https//saintantoine.aphp.fr/score/).

Known underlying immunodepression	No
Maximal temperature (°C)	Strictly greater than 39.4
Hepatomegaly	No
Splenomegaly	Yes
Lower hemoglobin level	Strictly greater than 92 g/L
Lower leukocyte count	Less than or equal to 5 g/L
Lower platelet count	Less than or equal to 110 g/L
Higher ferritin level (ng/ml)	Strictly greater than 6000
Higher triglyceride level (mmol/l)	Between 1.5 and 4
Lower fibrinogen level (g/L)	Strictly greater than 2.5
Higher ASAT/ALAT level (UI/l)	Greater than or equal to 30
Hemophagocytosis features on the bone marrow aspirate	No
	Calculate
HScore	209
Probability of having HS (%)	92.87735027549559