Case Report

Malignant Lymphoma in the Parasellar Region

Table 1

Clinical summary of 19 patients with PPL.

Age, sexClinical presentationEndocrine abnormalityPathologyTherapyOS (months)

28, M [16]HA, CN II/VB-cellChemo + Rd6, alive
49, M [12]HA, CN VIII, NysHypo, DI, PRLB-cellSten.d.
48, M [4]HA, CN VI, F, S&WL, nauseaB-cellAntituberculous therapy0.3, dead
73, F [13]HA, fatige, CN VIHypo, DI, PRLB-cellSte + Rd21.6, alive
53, M [11]HA, CN VIT-cellRd18, alive
48, M [3]HA, CN III/VIB-celln.d.n.d.
67, F [9]CN II/IIIHypoB-cellRd4M, alive
82, M [1]HA, CN IIHypo, DIB-cellRdn.d.
65, M [10]n.d.Hypo, PRLB-cellChemo0.5, alive
44, M [15]HA, CN IIB-cellChemo + MTx + Rdn.d.
86, F [31]F, S&WLHypo, DIB-cellChemo3, dead
15, M [14]F, S&WLHypo, DIB-cellChemo + HD MTx17, alive
74, M [8]CN II, F, S&WL, mental status changeHypo,B-cellRd1.5, dead
65, M [8]CN VI, retrobulbar painHypo,B-cellChemo24, dead
64, F [7]nausea, diarrhea, edemaHypo, DIB-cellChemo + Rd15, dead
47, M [5]F, S&WLHypo,T-cellChemo + i.t. MTx + Rd5, alive
26, M [6]HA, CN VI, F, S&WLHypo, PRLNK/T-cellChemo + i.t. MTx + Rd6, dead
49, F [2]HA, F, S&WLHypo, DI, PRLB-cellMTx48, alive
26, F [17]HA, F, S&WLHypo, PRLB-cell0.5, dead

Hypo: anterior hypopituitarism; B-cell: B-cell lymphoma; Chemo: chemotherapy; CN: cranial nerve palsy; DI: diabetes insipidus; F, S&WL: fever, night sweat, and weight loss; HA: headache; HD: high dose; i.t.: intrathecal; MTx: methotrexate; n.d.: not described; NK: NK cell lymphoma; Nys: nystagmus; OS: overall survival; PRL: hyperprolactinemia; Rd: radiotherapy; Ste: steroid; T-cell: T-cell lymphoma; —: none.