Case Report

Transhepatic Embolization of Congenital Intrahepatic Portosystemic Venous Shunts with Associated Aneurysms

Table 1

Summary of intrahepatic portosystemic shunts.

EtiologyIntrahepatic portosystemic shunts can be acquired (secondary to cirrhosis, trauma, or biopsy procedure) or congenital.

IncidenceAge of presentation young to middle age.

GenderBoth males and females are affected.

TreatmentEndovascular treatment (occlusion with coil or Amplatzer vascular plug), surgical ligation, or resection.

PrognosisMay be asymptomatic. Can resolve spontaneously. If symptomatic, there is good prognosis with treatment.

Findings on imagingDoppler US: presence of vascular structures connecting a portal branch to a hepatic vein with or without aneurysm formation.
Undulating triphasic waveform pattern in the portal vein similar to hepatic waveform.
CT/MRI with contrast: presence of vascular structures connecting a portal branch to a hepatic vein with or without aneurysm formation.