Case Report

Giant Cystic Pheochromocytoma with Low Risk of Malignancy: A Case Report and Literature Review

Table 2

A summary of reported giant pheochromocytomas with maximal diameter greater than 10 cm, arranged by largest to smallest maximum diameter. The weight was not recorded in many of the papers.

Author/yearSex/ageCountrySize (cm)/weight (g)LocationPresentationHistopathological evaluationMetastasis

Grissom et al./1979 [4]F/54USA45 × 25/3000+Left abdomenAsymptomaticUnknownNone
Costa et al./2008 [5]M/46Brazil30/unknownRight adrenalAbdominal painMalignantLiver
Basso et al./1996 [6]M/47Italy29 × 21 × 12/4050Left abdomenAsymptomaticMalignantNone
Karumanchery et al./2012 [7]F/85England28 × 16 × 13/2300Left abdomenLower back painUnknownNone
Current caseF/50Trinidad & Tobago27 × 18 × 12/3315Left abdomenLower back painLow risk of malignancyNone
Gupta et al./2016 [8]F/65India25 × 17 × 15/2750Left abdomenAsymptomaticBenignNone
Okuda et al./2013 [9]F/43Japan24 × 23 × 16/5900AbdomenVulva edemaUnknownNone
Suga et al./2000 [10]M/48Japan21 × 13 × 21/3900Left abdomenAsymptomaticUnknownNone
Terk et al./1993 [11]M/35USA21 × 20 × 11/2870Organ of ZuckerkandlDisproportionate abdominal girth, hypertensionUnknownNone
Soufi et al./2012 [12]F/17India21 × 15Right upper abdomenAsymptomaticMalignantNone
Arcos et al./2009 [13]F/36Canada21 × 17 × 11Left abdomenLower back painMalignantLymph node
Melegh et al./2002 [14]M/55Hungary20/unknownLeft renal hilusAsymptomaticUnknownNone
Korgali et al./2014 [15]M/63Turkey20 × 17 × 9/1736Left adrenal glandChest pain, sweating, nauseaMalignantRib
Ambati et al./2014 [16]F/77Canada19 × 18 × 12/2460Right retroperitoneumDyspneaBenignNone
Pan et al./2008 [17]M/46USA18 × 14 × 13/1450Left abdomenEpisodic hypertension and headacheUnknownUnknown
Uysal et al./2015 [18]M/37Turkey18 × 8 × 13Left abdomenHypertensionMalignantMulti
Sharma/2006 [19]M/55India17 × 12/850Right adrenal glandAsymptomaticBenignNone
Daughtry et al./1977 [20]M/53USA17/1150UnknownMild hypertensionUnknownUnknown
Gupta et al./2016 [8]M/40India16.4 × 14 /1836Left thyroid glandSevere hypertensionUnknownUnknown
Costa et al./2008 [5]F/43Brazil16Right upper abdomenAbdominal painMalignantUnknown
Jain and Agarwal /2002 [21]F/26India16 × 11Left abdomenAsymptomaticMalignantUnknown
Wu et al./2000 [22]F/49USA15 × 12 × 12Right upper abdomenAsymptomaticUnknownUnknown
Santarone et al./2008 [23]F/81Italy13Right upper abdomenHypertension, palpitation, sweatingUnknownUnknown
Sundahl et al./2016 [24]F/54Sweden12.5 × 10 × 3/204Right adrenal glandAsymptomaticBenignNone
Zhu et al./2014 [25]F/67Japan12.1 × 10.8Left adrenal glandDizziness, vomiting, and stomachacheUnknownNone
Ikegami et al./2009 [26]M/47Japan12 × 10AbdomenBack painUnknownUnknown
Li et al./2012 [27]M/56Canada12 × 11 × 11Right upper abdomenProgressive weight loss and nauseaBenignNone
Kakoki et al./2015 [28]M/70Japan12 × 11 × 8/530Left adrenal glandIleus after hypertension medicationBenignNone
Schnakenburg et al./1976 [29]M/12Ukraine12 × 10 × 9/1100Right abdomenHemihypertrophyMalignantLung, brain
Filippou et al./2003 [30]M/70Greece12 × 8 × 10Left abdomenAsymptomaticMalignantNone
Sarveswaran et al./2015 [31]F/59India11.2 × 9.6 × 9.8Right suprarenal regionUpper right abdominal discomfortUnknownUnknown
Chan et al./2000 [32]M/63China11 × 6.6 × 11Right suprarenal regionAsymptomaticMalignantBone, lung
Awada et al./2003 [33]F/26USA11 × 10 × 9Right adrenal glandDyspnea, paresthesia, chest pain, palpitationUnknownUnknown
Goldberg et al./2011 [34]F/27Canada10.5 × 10.6Right adrenal gland regionHeadaches, episodic palpitations, pallorUnknownUnknown
Antedomenico and Wascher/2005 [35]F/39USA10.5/782Left upper abdomenAbdominal painUnknownUnknown
Wang et al./2015 [36]F/36China10.3 × 9.3Left upper abdomenAbdominal painUnknownUnknown
Basiri and Radfar/2010 [37]M/53IranUnknown/3150Left abdomenAbdominal painBenignNone

M, male; F, female. , lymph nodes, right adrenal gland, lungs, and bones.