Evaluating Adult Cystic Fibrosis Care in BC: Disparities in Access to a Multidisciplinary Treatment Centre
Table 1
Baseline characteristics, CF complications, lung function, and nutritional status by travel time.
One-way travel time by automobile to SPH, min
value
<45 ()
45–150 ()
150–360 ()
>360 ()
Baseline characteristics
Mean age, yr (SD)
34 (11)
38 (15)
36 (14)
32 (10)
0.4
Male sex, (%)
52 (61%)
18 (64%)
21 (50%)
6 (46%)
0.4
Median age at diagnosis, yr (IQR)
5.5 (17.5)
5.5 (19)
2 (11)
1.5 (6)
0.3
F508del-CFTR homozygous, (%)
36 (42%)
9 (32%)
20 (48%)
6 (46%)
0.6
Chronic PsA+, (%)
33 (41%)
14 (54%)
18 (50%)
3 (27%)
0.4
CF complications
Pancreatic insufficiency, (%)
57 (68%)
20 (71%)
35 (83%)
9 (69%)
0.2
CFRD, (%)
26 (31%)
6 (21%)
11 (27%)
2 (17%)
0.7
Chronic sinusitis, (%)
49 (59%)
16 (57%)
27 (64%)
5 (42%)
0.6
Low BMD, (%)
29 (35%)
11 (39%)
14 (34%)
3 (25%)
0.8
Depression and/or anxiety, (%)
32 (38%)
8 (29%)
7 (17%)
2 (15%)
0.1
Lung function and nutritional status
FEV1% predicted (SD)
74 (27)
67 (28)
75 (26)
74 (23)
0.6
BMI, kg/m2 (SD)
23.7 (4.1)
22.5 (3.9)
23.5 (3.3)
23.2 (1.8)
0.5
Mean (standard deviation), median (intraquartile range), or (%). SD: standard deviation; BMD: bone mineral density; FEV1: forced expiratory volume in 1 second; BMI: body mass index; PsA+: P. aeruginosa isolates in >50% of annual sputum cultures; IQR: intraquartile range; CFRD: CF-related diabetes.