Research Article

Evaluating Adult Cystic Fibrosis Care in BC: Disparities in Access to a Multidisciplinary Treatment Centre

Table 1

Baseline characteristics, CF complications, lung function, and nutritional status by travel time.

One-way travel time by automobile to SPH, min value
<45 ()45–150 ()150–360 ()>360 ()

Baseline characteristics
 Mean age, yr (SD)34 (11)38 (15)36 (14)32 (10)0.4
 Male sex, (%)52 (61%)18 (64%)21 (50%)6 (46%)0.4
 Median age at diagnosis, yr (IQR)5.5 (17.5)5.5 (19)2 (11)1.5 (6)0.3
 F508del-CFTR homozygous, (%)36 (42%)9 (32%)20 (48%)6 (46%)0.6
 Chronic PsA+, (%)33 (41%)14 (54%)18 (50%)3 (27%)0.4
CF complications
 Pancreatic insufficiency, (%)57 (68%)20 (71%)35 (83%)9 (69%)0.2
 CFRD, (%)26 (31%)6 (21%)11 (27%)2 (17%)0.7
 Chronic sinusitis, (%)49 (59%)16 (57%)27 (64%)5 (42%)0.6
 Low BMD, (%)29 (35%)11 (39%)14 (34%)3 (25%)0.8
 Depression and/or anxiety, (%)32 (38%)8 (29%)7 (17%)2 (15%)0.1
Lung function and nutritional status
 FEV1% predicted (SD)74 (27) 67 (28)75 (26)74 (23)0.6
 BMI, kg/m2 (SD)23.7 (4.1)22.5 (3.9)23.5 (3.3)23.2 (1.8)0.5

Mean (standard deviation), median (intraquartile range), or (%).
SD: standard deviation; BMD: bone mineral density; FEV1: forced expiratory volume in 1 second; BMI: body mass index; PsA+: P. aeruginosa isolates in >50% of annual sputum cultures; IQR: intraquartile range; CFRD: CF-related diabetes.