Research Article

The Impact of Optical Coherence Tomography in the Early Identification of Children with Sickle Cell Retinopathy

Table 3

The ocular findings and hemoglobin genotypes among the studied patients.

HB genotype(no)Fundus examinationOCTOCTA
Deep retinal capillary plexusSuperficial retinal capillary plexus

Hb SS (8)2 patientsNormalNormalNormalNormal
1 patientBilaterally abnormalBilateral macular atrophyBilateral flow voidBilateral flow void
2 patientsBilaterally abnormalBilateral macular atrophyBilateral flow voidNormal
2 patientsBilaterally abnormalUnilateral macular atrophyUnilateral flow voidNormal
1 patientNormalUnilateral macular atrophyUnilateral flow voidNormal
Hb SC (3)1 patientUnilaterally abnormalUnilateral macular atrophyUnilateral macular atrophyUnilateral flow void
2 patientsNormalNormalNormalNormal
Hb SB+ (3)3 patientsNormalNormalNormalNormal
Hb SB0 (1)1 patientUnilaterally abnormalNormalNormalUnilateral flow void