Application of the New Classification on Patients with a Disorder of Sex Development in Indonesia

Table 4

Final classification.

DSD classification	Number of patients	Total
46, XX DSD
Disorder of androgen excess, other	2
Disorder of androgen excess, 21 hydroxylase deficiency	15
Defect of mullerian development, other	4
Disorder of gonadal development, ovotesticular DSD	1	22
46, XY DSD
Disorder of gonadal development, other	9
Disorder of androgen action, PAIS	12
Disorder of androgen action, other	17
Male undermasculinisation of unknown aetiology	20	58
Chromosomal DSD
46 XX/46 XY DSD, disorder of gonadal development,; ovotesticular DSD	1
47 XXY DSD, disorder of gonadal development, other	3
45X/46XY DSD, disorder of gonadal development, other	2
Other, disorder of gonadal development, other	2	8