Clinical Study
Long-Term Effect of Enzyme Replacement Therapy with Fabry Disease
Table 2
Criteria for improvement. In Japan, outcome of therapy has been classified as follows.
| (1) Healing | (1) When hearing level at 0.25, 0.5, 1, 2, 4 kHz returned to less than 20 dB. (2) When hearing level returned to the same as that in the other side. | (2) Marked recovery | When the value of the arithmetic means of the hearing levels at the five above-mentioned frequencies was greater than 30 dB. | (3) Recovery | When the value of the arithmetic means of the hearing levels at the five above-mentioned frequencies was less than 30 dB and greater than 10 dB. | (4) Unchangeable | When the value of the arithmetic means of the hearing levels at the five above-mentioned frequencies was less than 10 dB. (Including exacerbation) |
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