Genetic and Clinical Features of Multiple Endocrine Neoplasia Types 1 and 2

Table 2

Prevalence of tumoral diseases in MEN 2 syndromes.

Phenotype	MTC (%)	PHEO (%)	HPT (%)	Nonendocrinological associated pathologies (%)
MEN 2A	95	50	25	Cutaneous lichen amyloidosis (10%)
				Hirschsprung’s disease (2%)
MEN 2B	95	50		Mucosal neuromas (100%)
				Marfanoid habitus (100%)
				Ganglioneuromatosis of the gastrointestinal tract (60%)
FMTC	100