Research Article

Novel Echocardiographic Metrics Predict Tricuspid Insufficiency in Pediatric Ebstein Anomaly

Table 1

Baseline characteristics.

VariablesValues

Age (months), median (IQR)39.9 (23.4–86.4)
Male, n (%)27 (36.5)
Weight (kg), median (IQR)14.85 (11–25)
Height (cm), median (IQR)96 (85–122)
BSA (m2), median (IQR)0.59 (0.47–0.88)
ASD, n (%)41 (55.4)
VSD, n (%)8 (10.8)
Left ventricular ejection fraction (%), mean ± SD70.8 ± 7.9
Z-score of the tricuspid annulus diameter, median (IQR)7.3 (3.7–9.9)
RV FAC (%), median (IQR)46.0 (40.1–50.8)
ALM (degrees), mean ± SD43.8 ± 12.4
ALL-I (cm/m2), median (IQR)6.1 (4.1–8.1)
Carpentier type, n (%)
 A47 (63.5)
 B26 (35.1)
 C1 (1.4)
 D0 (0)
GOSH score, n (%)
 <0.514 (18.9)
 0.5–0.9945 (60.8)
 1–1.4911 (14.9)
 ≥1.54 (5.4)
Preoperative TR severity, n (%)
 Mild4 (5.4)
 Mild-moderate7 (9.5)
 Moderate25 (33.8)
 Moderate-severe16 (21.6)
 Severe22 (29.7)

Abbreviations: ALM, anterior leaflet mobility; ALL-I, anterior leaflet length indexed to body surface area; ASD, atrial septal defect; BSA, body surface area; RV FAC, right ventricle fractional area change; TR, tricuspid regurgitation; VSD, ventricular septal defect.