Case Report

Anesthetic Management and Neuromonitoring in a Patient with Very Long-Chain Acyl-Coenzyme A Dehydrogenase Deficiency Undergoing Scoliosis Surgery: A Case Report and Review of Literature

Table 2

Review of literature on VLCADD cases, sorted by year.

Author, yearNumber of casesPatient age (s)Type of surgeryAnesthetic techniqueAdverse events

Bo et al. [17], 202111.5OrchiopexyGeneral anesthesia: induction with fentanyl, rocuronium, and thiopental. Maintenance with sevofluraneNone
Yuasa et al. [5], 2020137Laparoscopic ovarian cystectomyGeneral anesthesia: induction with midazolam, remifentanil, and thiamylal. Maintenance with desflurane, remifentanilNone
Hess et al. [13], 201813AdenotonsillectomyGeneral anesthesia with laryngeal mask airway: induction and maintenance with sevofluraneNone
Welsink-Karssies et al. [14], 2016124Neck cyst removalGeneral anesthesia: induction with remifentanil, rocuronium, and thiopental. Maintenance with remifentanil and sevofluraneNone
Iwata et al. [18], 2012128Hysteroscopic myomectomyGeneral anesthesia: induction with remifentanil, rocuronium, and thiopental. Maintenance with remifentanil and sevofluraneSlight elevation of lactate intraoperatively, elevated CK on postoperative day 2
Vellekoop et al. [12], 201128 months, 11 yearsPercutaneous endoscopic gastrostomy, placement of intravenous access device (PAC)Case 1: general anesthesia: induction and maintenance with sevoflurane. Case 2: general anesthesia: induction with fentanyl and propofol. Maintenance with sevofluraneCase 1: rhabdomyolysis with maximum CK of 163,610U/L and myoglobinuria. Case 2: none
Schmidt et al. [19], 200918 monthsDiagnostic muscle biopsy and percutaneous endoscopic gastrostomy placementTotal intravenous anesthesia: induction with mivacurium, remifentanil, and thiopentone. Maintenance with midazolam and remifentanilNone
Steiner et al. [20], 200219CircumcisionGeneral anesthesia with laryngeal mask airway: induction with midazolam and thiopental. Maintenance with alfentanil and midazolamDelayed awakening (3 hours postoperatively)