Clinical Study
Inflammatory Lung Disease in Rett Syndrome
Figure 3
Lymphocytic bronchiolitis and desquamative alveolitis in Mecp2 null mice. (a) Wild-type mouse lung: normal histological features (magnification 25x), (b) Mecp2 null mouse: peribronchiolar lymphocyticinfiltrate (magnification 50x), (c) Mecp2 null mouse lung: desquamative alveolitis with mild amount of alveolar exudate (50x), and (d) Mecp2 null mouse lung: terminal bronchiolitis at higher magnification (200x) lymphocytes and histiocytes infiltrates outside and inside thickened terminal bronchioles, with a resulting picture of lymphocytic bronchiolitis.