Research Article

Long-Term Outcomes of Behçet’s Syndrome-Related Uveitis: A Monocentric Italian Experience

Table 1

Demographic and extraocular features of our cohort at disease onset and throughout the course of Behçet’s syndrome.

Demographic features expressed in years

Female/male23/24
Age
Age at BS onset
Age at uveitis onset
Uveitis duration
HLA-B5127/47 (57.45%)
Clinical features at onset(%)
Uveitis31 (65.96%)
Oral aphthosis34 (72.34%)
Genital aphthosis9 (19.15%)
Erythema nodosum2 (4.25%)
Pseudofollicular lesions7 (14.89%)
CNS involvement2 (4.25%)
Gastrointestinal involvement4 (8.51%)
Vascular involvement2 (4.25%)
Clinical features throughout BS course(%)
Oral aphthosis46 (97.87%)
Genital aphthosis19 (40.43%)
Erythema nodosum8 (17.02%)
Pseudofollicular lesions24 (51.06%)
CNS involvement8 (17.02%)
Gastrointestinal involvement15 (31.91%)
Vascular involvement12 (25.53%)

List of abbreviations: BS: Behçet’s syndrome; CNS: central nervous system; HLA: human leukocyte antigen; IQR: interquartile range; SD: standard deviation.